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Packageus.nlm.vsac
Resource TypeValueSet
IdValueSet-2.16.840.1.113883.3.526.2.1643.json
FHIR VersionR4
Sourcehttps://vsac.nlm.nih.gov/valueset/2.16.840.1.113883.3.526.2.1643/expansion
URLhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.526.2.1643
Version20250125
Statusactive
Date2025-01-25T01:09:35-05:00
NameDegenerationOfMaculaAndPosteriorPole
TitleDegeneration of Macula and Posterior Pole
Realmus
Authorityhl7
Purpose(Clinical Focus: The purpose of this value set is to represent concepts of a diagnosis of degeneration of macula and posterior pole.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of macula and/or posterior pole degenerations, including age-related degenerations, macular cyst, maculopathy, macular puckering, macular hole, atrophy or dystrophy of macula.),(Exclusion Criteria: Excludes concepts that represent a diagnosis for 'unspecified eye.')

Resources that use this resource

ValueSet
2.16.840.1.113883.3.526.3.1453Degeneration of Macula and Posterior Pole

Resources that this resource uses

CodeSystem
sctSNOMED codes used in this IG

Narrative

No narrative content found in resource


Source1

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      "valueDate": "2025-05-12"
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  "version": "20250125",
  "name": "DegenerationOfMaculaAndPosteriorPole",
  "title": "Degeneration of Macula and Posterior Pole",
  "status": "active",
  "date": "2025-01-25T01:09:35-05:00",
  "publisher": "American Academy of Ophthalmology Steward",
  "jurisdiction": [
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      "coding": [
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          "code": "US"
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    "include": [
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        "concept": [
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            "code": "1187639002",
            "display": "Martinique crinkled retinal pigment epitheliopathy (disorder)"
          },
          {
            "code": "1231253003",
            "display": "Macular hole due to degenerative progressive high myopia (disorder)"
          },
          {
            "code": "1285507004",
            "display": "Nonexudative neovascular age-related macular degeneration (disorder)"
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          {
            "code": "1285513008",
            "display": "Lamellar macular hole (disorder)"
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          {
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            "display": "Pachychoroid neovasculopathy (disorder)"
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            "code": "1285589003",
            "display": "Nongeographic atrophy of macula lutea (disorder)"
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          {
            "code": "1296526000",
            "display": "Disciform macular degeneration (disorder)"
          },
          {
            "code": "1338026004",
            "display": "Disorder of macula of retina caused by radiation (disorder)"
          },
          {
            "code": "1338027008",
            "display": "Disorder of macula of retina due to and following radiotherapy (disorder)"
          },
          {
            "code": "14046000",
            "display": "Cystoid macular retinal degeneration (disorder)"
          },
          {
            "code": "15628531000119107",
            "display": "Fundus flavimaculatus of right eye (disorder)"
          },
          {
            "code": "15628571000119105",
            "display": "Fundus flavimaculatus of left eye (disorder)"
          },
          {
            "code": "15628611000119101",
            "display": "Fundus flavimaculatus of bilateral eyes (disorder)"
          },
          {
            "code": "15628771000119100",
            "display": "Forster-Fuchs spot of right eye (disorder)"
          },
          {
            "code": "15628811000119100",
            "display": "Forster-Fuchs spot of left eye (disorder)"
          },
          {
            "code": "15628851000119104",
            "display": "Forster-Fuchs spot of bilateral eyes (disorder)"
          },
          {
            "code": "15631531000119100",
            "display": "Scarred macula of bilateral eyes (disorder)"
          },
          {
            "code": "15631611000119106",
            "display": "Scarred macula of right eye (disorder)"
          },
          {
            "code": "15639131000119107",
            "display": "Macular edema of retina of right eye (disorder)"
          },
          {
            "code": "15639181000119108",
            "display": "Macular edema of retina of left eye (disorder)"
          },
          {
            "code": "15639231000119102",
            "display": "Macular edema of retina of bilateral eyes (disorder)"
          },
          {
            "code": "16320791000119106",
            "display": "Myopic macular degeneration of bilateral eyes (disorder)"
          },
          {
            "code": "16320831000119100",
            "display": "Myopic macular degeneration of right eye (disorder)"
          },
          {
            "code": "16320871000119102",
            "display": "Myopic macular degeneration of left eye (disorder)"
          },
          {
            "code": "18410006",
            "display": "Scarred macula (disorder)"
          },
          {
            "code": "193350004",
            "display": "Advanced maculopathy due to diabetes mellitus (disorder)"
          },
          {
            "code": "193387007",
            "display": "Cystoid macular edema (disorder)"
          },
          {
            "code": "193410003",
            "display": "Sorsby pseudoinflammatory fundus dystrophy (disorder)"
          },
          {
            "code": "232006002",
            "display": "Macular hole (disorder)"
          },
          {
            "code": "232013002",
            "display": "Macular retinoschisis (disorder)"
          },
          {
            "code": "232014008",
            "display": "Macular and peripheral retinoschisis (disorder)"
          },
          {
            "code": "232020009",
            "display": "Disorder of macula due to diabetes mellitus (disorder)"
          },
          {
            "code": "232049001",
            "display": "Adult vitelliform macular dystrophy (disorder)"
          },
          {
            "code": "232050001",
            "display": "Bull's eye macular dystrophy (disorder)"
          },
          {
            "code": "232051002",
            "display": "Pattern dystrophy of macula (disorder)"
          },
          {
            "code": "232071006",
            "display": "Occult neovascularization of macula (disorder)"
          },
          {
            "code": "232072004",
            "display": "Forster-Fuchs' spot (disorder)"
          },
          {
            "code": "247146001",
            "display": "Macular pigment deposit (disorder)"
          },
          {
            "code": "247147005",
            "display": "Macular diffuse atrophy (disorder)"
          },
          {
            "code": "247149008",
            "display": "Macular choroidal sclerosis (disorder)"
          },
          {
            "code": "247158001",
            "display": "Macular pigment epithelial detachment (disorder)"
          },
          {
            "code": "247159009",
            "display": "Macular retinal pigment epithelium tear (disorder)"
          },
          {
            "code": "247172005",
            "display": "Retinal macular break (disorder)"
          },
          {
            "code": "247200005",
            "display": "Choroidal atrophy (finding)"
          },
          {
            "code": "264633009",
            "display": "Drusen stage macular degeneration (disorder)"
          },
          {
            "code": "267612009",
            "display": "Degeneration of macula due to cyst, hole or pseudohole (disorder)"
          },
          {
            "code": "267718000",
            "display": "Age-related macular degeneration (disorder)"
          },
          {
            "code": "276436007",
            "display": "Hereditary macular dystrophy (disorder)"
          },
          {
            "code": "312701008",
            "display": "Impending macular hole (disorder)"
          },
          {
            "code": "312702001",
            "display": "Full thickness macular hole stage II (disorder)"
          },
          {
            "code": "312703006",
            "display": "Full thickness macular hole stage III (disorder)"
          },
          {
            "code": "312704000",
            "display": "Full thickness macular hole stage IV (disorder)"
          },
          {
            "code": "312898002",
            "display": "Myopic macular degeneration (disorder)"
          },
          {
            "code": "312899005",
            "display": "Fibrovascular macular scar (disorder)"
          },
          {
            "code": "312901001",
            "display": "Vitreomacular traction syndrome (disorder)"
          },
          {
            "code": "312902008",
            "display": "Macular pseudohole (disorder)"
          },
          {
            "code": "312911008",
            "display": "Clinically significant macular edema (disorder)"
          },
          {
            "code": "312912001",
            "display": "Macular edema due to diabetes mellitus (disorder)"
          },
          {
            "code": "312913006",
            "display": "Ischemic maculopathy (disorder)"
          },
          {
            "code": "312920004",
            "display": "Postoperative cystoid macular edema (disorder)"
          },
          {
            "code": "312921000",
            "display": "Autosomal dominant cystoid macular edema (disorder)"
          },
          {
            "code": "312922007",
            "display": "Uveitis related cystoid macular edema (disorder)"
          },
          {
            "code": "312925009",
            "display": "North Carolina macular dystrophy (disorder)"
          },
          {
            "code": "312999006",
            "display": "Disorder of macula of retina (disorder)"
          },
          {
            "code": "313002004",
            "display": "Acute macular neuroretinitis (disorder)"
          },
          {
            "code": "314010006",
            "display": "Diffuse exudative maculopathy due to diabetes mellitus (disorder)"
          },
          {
            "code": "314011005",
            "display": "Focal exudative maculopathy due to diabetes mellitus (disorder)"
          },
          {
            "code": "314014002",
            "display": "Ischemic maculopathy due to diabetes mellitus (disorder)"
          },
          {
            "code": "314015001",
            "display": "Mixed maculopathy due to diabetes mellitus (disorder)"
          },
          {
            "code": "314427006",
            "display": "Drusen plus pigment change stage macular degeneration (disorder)"
          },
          {
            "code": "331821000119106",
            "display": "Toxic disorder of macula lutea of right eye (disorder)"
          },
          {
            "code": "335531000119109",
            "display": "Cystoid macular degeneration of right retina (disorder)"
          },
          {
            "code": "337441000119109",
            "display": "Toxic disorder of macula lutea of left eye (disorder)"
          },
          {
            "code": "341141000119106",
            "display": "Cystoid macular degeneration of left retina (disorder)"
          },
          {
            "code": "343231000119106",
            "display": "Toxic maculopathy of bilateral eyes (disorder)"
          },
          {
            "code": "346401000119108",
            "display": "Cystoid macular degeneration of bilateral retinas (disorder)"
          },
          {
            "code": "37231002",
            "display": "Macular retinal edema (disorder)"
          },
          {
            "code": "399864000",
            "display": "Macular edema not clinically significant due to diabetes mellitus (disorder)"
          },
          {
            "code": "399872003",
            "display": "Severe nonproliferative retinopathy with clinically significant macular edema due to diabetes mellitus (disorder)"
          },
          {
            "code": "399874002",
            "display": "High risk proliferative retinopathy with clinically significant macula edema due to diabetes mellitus (disorder)"
          },
          {
            "code": "399875001",
            "display": "Non-high-risk proliferative retinopathy with clinically significant macular edema due to diabetes mellitus (disorder)"
          },
          {
            "code": "399877009",
            "display": "Very severe nonproliferative retinopathy with clinically significant macular edema due to diabetes mellitus (disorder)"
          },
          {
            "code": "4041005",
            "display": "Congenital anomaly of macula (disorder)"
          },
          {
            "code": "414173003",
            "display": "Exudative age-related macular degeneration (disorder)"
          },
          {
            "code": "414875008",
            "display": "Nonexudative age-related macular degeneration (disorder)"
          },
          {
            "code": "418918009",
            "display": "Macular infarction (disorder)"
          },
          {
            "code": "420030000",
            "display": "Serous macular detachment (disorder)"
          },
          {
            "code": "420486006",
            "display": "Exudative maculopathy due to type 1 diabetes mellitus (disorder)"
          },
          {
            "code": "421779007",
            "display": "Exudative maculopathy due to type 2 diabetes mellitus (disorder)"
          },
          {
            "code": "422338006",
            "display": "Degenerative disorder of macula (disorder)"
          },
          {
            "code": "423084001",
            "display": "Macular exudate (disorder)"
          },
          {
            "code": "425622004",
            "display": "Scar of macula following trauma (disorder)"
          },
          {
            "code": "429449002",
            "display": "Congenital hypoplasia of fovea centralis (disorder)"
          },
          {
            "code": "432789001",
            "display": "Noncystoid edema of macula of retina (disorder)"
          },
          {
            "code": "44115007",
            "display": "Toxic maculopathy (disorder)"
          },
          {
            "code": "443437004",
            "display": "Full thickness hole of macula lutea (disorder)"
          },
          {
            "code": "47673003",
            "display": "Fundus flavimaculatus (disorder)"
          },
          {
            "code": "677851000119101",
            "display": "Macular hole of bilateral eyes (disorder)"
          },
          {
            "code": "677861000119104",
            "display": "Full thickness macular hole of bilateral eyes (disorder)"
          },
          {
            "code": "677871000119105",
            "display": "Partial thickness macular hole of bilateral eyes (disorder)"
          },
          {
            "code": "677881000119108",
            "display": "Macular pseudohole of bilateral eyes (disorder)"
          },
          {
            "code": "677901000119105",
            "display": "Macular hole of left eye (disorder)"
          },
          {
            "code": "677911000119108",
            "display": "Full thickness macular hole of left eye (disorder)"
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          {
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          {
            "code": "677931000119103",
            "display": "Macular pseudohole of left eye (disorder)"
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          {
            "code": "677951000119109",
            "display": "Macular hole of right eye (disorder)"
          },
          {
            "code": "677961000119106",
            "display": "Full thickness macular hole of right eye (disorder)"
          },
          {
            "code": "677971000119100",
            "display": "Partial thickness macular hole of right eye (disorder)"
          },
          {
            "code": "677981000119102",
            "display": "Macular pseudohole of right eye (disorder)"
          },
          {
            "code": "70099003",
            "display": "Stargardt's disease (disorder)"
          },
          {
            "code": "725590001",
            "display": "Butterfly-shaped pigmentary macular dystrophy (disorder)"
          },
          {
            "code": "737273002",
            "display": "Degeneration of posterior pole of eye (disorder)"
          },
          {
            "code": "769244003",
            "display": "Disorder of right macula due to diabetes mellitus (disorder)"
          },
          {
            "code": "769245002",
            "display": "Disorder of left macula due to diabetes mellitus (disorder)"
          },
          {
            "code": "770097006",
            "display": "Clinically significant macular edema due to diabetes mellitus (disorder)"
          },
          {
            "code": "774010000",
            "display": "Scarred macula of left eye (disorder)"
          },
          {
            "code": "789220007",
            "display": "Atrophy of macula lutea (disorder)"
          },
          {
            "code": "860721006",
            "display": "Disorder of macula of bilateral eyes due to diabetes mellitus (disorder)"
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  "expansion": {
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    "timestamp": "2025-05-23T22:40:15-04:00",
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