FHIR IG analytics
| Package | us.nlm.vsac |
| Resource Type | ValueSet |
| Id | ValueSet-2.16.840.1.113883.3.526.2.1643.json |
| FHIR Version | R4 |
| Source | https://vsac.nlm.nih.gov/valueset/2.16.840.1.113883.3.526.2.1643/expansion |
| URL | http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.526.2.1643 |
| Version | 20250125 |
| Status | active |
| Date | 2025-01-25T01:09:35-05:00 |
| Name | DegenerationOfMaculaAndPosteriorPole |
| Title | Degeneration of Macula and Posterior Pole |
| Realm | us |
| Authority | hl7 |
| Purpose | (Clinical Focus: The purpose of this value set is to represent concepts of a diagnosis of degeneration of macula and posterior pole.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of macula and/or posterior pole degenerations, including age-related degenerations, macular cyst, maculopathy, macular puckering, macular hole, atrophy or dystrophy of macula.),(Exclusion Criteria: Excludes concepts that represent a diagnosis for 'unspecified eye.') |
Resources that use this resource
Resources that this resource uses
| CodeSystem |
| sct | SNOMED codes used in this IG |
Narrative
No narrative content found in resource
Source1
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"name": "DegenerationOfMaculaAndPosteriorPole",
"title": "Degeneration of Macula and Posterior Pole",
"status": "active",
"date": "2025-01-25T01:09:35-05:00",
"publisher": "American Academy of Ophthalmology Steward",
"jurisdiction": [
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"purpose": "(Clinical Focus: The purpose of this value set is to represent concepts of a diagnosis of degeneration of macula and posterior pole.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of macula and/or posterior pole degenerations, including age-related degenerations, macular cyst, maculopathy, macular puckering, macular hole, atrophy or dystrophy of macula.),(Exclusion Criteria: Excludes concepts that represent a diagnosis for 'unspecified eye.')",
"compose": {
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{
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"concept": [
{
"code": "1187639002",
"display": "Martinique crinkled retinal pigment epitheliopathy (disorder)"
},
{
"code": "1231253003",
"display": "Macular hole due to degenerative progressive high myopia (disorder)"
},
{
"code": "1285507004",
"display": "Nonexudative neovascular age-related macular degeneration (disorder)"
},
{
"code": "1285513008",
"display": "Lamellar macular hole (disorder)"
},
{
"code": "1285540008",
"display": "Pachychoroid neovasculopathy (disorder)"
},
{
"code": "1285589003",
"display": "Nongeographic atrophy of macula lutea (disorder)"
},
{
"code": "1296526000",
"display": "Disciform macular degeneration (disorder)"
},
{
"code": "1338026004",
"display": "Disorder of macula of retina caused by radiation (disorder)"
},
{
"code": "1338027008",
"display": "Disorder of macula of retina due to and following radiotherapy (disorder)"
},
{
"code": "14046000",
"display": "Cystoid macular retinal degeneration (disorder)"
},
{
"code": "15628531000119107",
"display": "Fundus flavimaculatus of right eye (disorder)"
},
{
"code": "15628571000119105",
"display": "Fundus flavimaculatus of left eye (disorder)"
},
{
"code": "15628611000119101",
"display": "Fundus flavimaculatus of bilateral eyes (disorder)"
},
{
"code": "15628771000119100",
"display": "Forster-Fuchs spot of right eye (disorder)"
},
{
"code": "15628811000119100",
"display": "Forster-Fuchs spot of left eye (disorder)"
},
{
"code": "15628851000119104",
"display": "Forster-Fuchs spot of bilateral eyes (disorder)"
},
{
"code": "15631531000119100",
"display": "Scarred macula of bilateral eyes (disorder)"
},
{
"code": "15631611000119106",
"display": "Scarred macula of right eye (disorder)"
},
{
"code": "15639131000119107",
"display": "Macular edema of retina of right eye (disorder)"
},
{
"code": "15639181000119108",
"display": "Macular edema of retina of left eye (disorder)"
},
{
"code": "15639231000119102",
"display": "Macular edema of retina of bilateral eyes (disorder)"
},
{
"code": "16320791000119106",
"display": "Myopic macular degeneration of bilateral eyes (disorder)"
},
{
"code": "16320831000119100",
"display": "Myopic macular degeneration of right eye (disorder)"
},
{
"code": "16320871000119102",
"display": "Myopic macular degeneration of left eye (disorder)"
},
{
"code": "18410006",
"display": "Scarred macula (disorder)"
},
{
"code": "193350004",
"display": "Advanced maculopathy due to diabetes mellitus (disorder)"
},
{
"code": "193387007",
"display": "Cystoid macular edema (disorder)"
},
{
"code": "193410003",
"display": "Sorsby pseudoinflammatory fundus dystrophy (disorder)"
},
{
"code": "232006002",
"display": "Macular hole (disorder)"
},
{
"code": "232013002",
"display": "Macular retinoschisis (disorder)"
},
{
"code": "232014008",
"display": "Macular and peripheral retinoschisis (disorder)"
},
{
"code": "232020009",
"display": "Disorder of macula due to diabetes mellitus (disorder)"
},
{
"code": "232049001",
"display": "Adult vitelliform macular dystrophy (disorder)"
},
{
"code": "232050001",
"display": "Bull's eye macular dystrophy (disorder)"
},
{
"code": "232051002",
"display": "Pattern dystrophy of macula (disorder)"
},
{
"code": "232071006",
"display": "Occult neovascularization of macula (disorder)"
},
{
"code": "232072004",
"display": "Forster-Fuchs' spot (disorder)"
},
{
"code": "247146001",
"display": "Macular pigment deposit (disorder)"
},
{
"code": "247147005",
"display": "Macular diffuse atrophy (disorder)"
},
{
"code": "247149008",
"display": "Macular choroidal sclerosis (disorder)"
},
{
"code": "247158001",
"display": "Macular pigment epithelial detachment (disorder)"
},
{
"code": "247159009",
"display": "Macular retinal pigment epithelium tear (disorder)"
},
{
"code": "247172005",
"display": "Retinal macular break (disorder)"
},
{
"code": "247200005",
"display": "Choroidal atrophy (finding)"
},
{
"code": "264633009",
"display": "Drusen stage macular degeneration (disorder)"
},
{
"code": "267612009",
"display": "Degeneration of macula due to cyst, hole or pseudohole (disorder)"
},
{
"code": "267718000",
"display": "Age-related macular degeneration (disorder)"
},
{
"code": "276436007",
"display": "Hereditary macular dystrophy (disorder)"
},
{
"code": "312701008",
"display": "Impending macular hole (disorder)"
},
{
"code": "312702001",
"display": "Full thickness macular hole stage II (disorder)"
},
{
"code": "312703006",
"display": "Full thickness macular hole stage III (disorder)"
},
{
"code": "312704000",
"display": "Full thickness macular hole stage IV (disorder)"
},
{
"code": "312898002",
"display": "Myopic macular degeneration (disorder)"
},
{
"code": "312899005",
"display": "Fibrovascular macular scar (disorder)"
},
{
"code": "312901001",
"display": "Vitreomacular traction syndrome (disorder)"
},
{
"code": "312902008",
"display": "Macular pseudohole (disorder)"
},
{
"code": "312911008",
"display": "Clinically significant macular edema (disorder)"
},
{
"code": "312912001",
"display": "Macular edema due to diabetes mellitus (disorder)"
},
{
"code": "312913006",
"display": "Ischemic maculopathy (disorder)"
},
{
"code": "312920004",
"display": "Postoperative cystoid macular edema (disorder)"
},
{
"code": "312921000",
"display": "Autosomal dominant cystoid macular edema (disorder)"
},
{
"code": "312922007",
"display": "Uveitis related cystoid macular edema (disorder)"
},
{
"code": "312925009",
"display": "North Carolina macular dystrophy (disorder)"
},
{
"code": "312999006",
"display": "Disorder of macula of retina (disorder)"
},
{
"code": "313002004",
"display": "Acute macular neuroretinitis (disorder)"
},
{
"code": "314010006",
"display": "Diffuse exudative maculopathy due to diabetes mellitus (disorder)"
},
{
"code": "314011005",
"display": "Focal exudative maculopathy due to diabetes mellitus (disorder)"
},
{
"code": "314014002",
"display": "Ischemic maculopathy due to diabetes mellitus (disorder)"
},
{
"code": "314015001",
"display": "Mixed maculopathy due to diabetes mellitus (disorder)"
},
{
"code": "314427006",
"display": "Drusen plus pigment change stage macular degeneration (disorder)"
},
{
"code": "331821000119106",
"display": "Toxic disorder of macula lutea of right eye (disorder)"
},
{
"code": "335531000119109",
"display": "Cystoid macular degeneration of right retina (disorder)"
},
{
"code": "337441000119109",
"display": "Toxic disorder of macula lutea of left eye (disorder)"
},
{
"code": "341141000119106",
"display": "Cystoid macular degeneration of left retina (disorder)"
},
{
"code": "343231000119106",
"display": "Toxic maculopathy of bilateral eyes (disorder)"
},
{
"code": "346401000119108",
"display": "Cystoid macular degeneration of bilateral retinas (disorder)"
},
{
"code": "37231002",
"display": "Macular retinal edema (disorder)"
},
{
"code": "399864000",
"display": "Macular edema not clinically significant due to diabetes mellitus (disorder)"
},
{
"code": "399872003",
"display": "Severe nonproliferative retinopathy with clinically significant macular edema due to diabetes mellitus (disorder)"
},
{
"code": "399874002",
"display": "High risk proliferative retinopathy with clinically significant macula edema due to diabetes mellitus (disorder)"
},
{
"code": "399875001",
"display": "Non-high-risk proliferative retinopathy with clinically significant macular edema due to diabetes mellitus (disorder)"
},
{
"code": "399877009",
"display": "Very severe nonproliferative retinopathy with clinically significant macular edema due to diabetes mellitus (disorder)"
},
{
"code": "4041005",
"display": "Congenital anomaly of macula (disorder)"
},
{
"code": "414173003",
"display": "Exudative age-related macular degeneration (disorder)"
},
{
"code": "414875008",
"display": "Nonexudative age-related macular degeneration (disorder)"
},
{
"code": "418918009",
"display": "Macular infarction (disorder)"
},
{
"code": "420030000",
"display": "Serous macular detachment (disorder)"
},
{
"code": "420486006",
"display": "Exudative maculopathy due to type 1 diabetes mellitus (disorder)"
},
{
"code": "421779007",
"display": "Exudative maculopathy due to type 2 diabetes mellitus (disorder)"
},
{
"code": "422338006",
"display": "Degenerative disorder of macula (disorder)"
},
{
"code": "423084001",
"display": "Macular exudate (disorder)"
},
{
"code": "425622004",
"display": "Scar of macula following trauma (disorder)"
},
{
"code": "429449002",
"display": "Congenital hypoplasia of fovea centralis (disorder)"
},
{
"code": "432789001",
"display": "Noncystoid edema of macula of retina (disorder)"
},
{
"code": "44115007",
"display": "Toxic maculopathy (disorder)"
},
{
"code": "443437004",
"display": "Full thickness hole of macula lutea (disorder)"
},
{
"code": "47673003",
"display": "Fundus flavimaculatus (disorder)"
},
{
"code": "677851000119101",
"display": "Macular hole of bilateral eyes (disorder)"
},
{
"code": "677861000119104",
"display": "Full thickness macular hole of bilateral eyes (disorder)"
},
{
"code": "677871000119105",
"display": "Partial thickness macular hole of bilateral eyes (disorder)"
},
{
"code": "677881000119108",
"display": "Macular pseudohole of bilateral eyes (disorder)"
},
{
"code": "677901000119105",
"display": "Macular hole of left eye (disorder)"
},
{
"code": "677911000119108",
"display": "Full thickness macular hole of left eye (disorder)"
},
{
"code": "677921000119101",
"display": "Partial thickness macular hole of left eye (disorder)"
},
{
"code": "677931000119103",
"display": "Macular pseudohole of left eye (disorder)"
},
{
"code": "677951000119109",
"display": "Macular hole of right eye (disorder)"
},
{
"code": "677961000119106",
"display": "Full thickness macular hole of right eye (disorder)"
},
{
"code": "677971000119100",
"display": "Partial thickness macular hole of right eye (disorder)"
},
{
"code": "677981000119102",
"display": "Macular pseudohole of right eye (disorder)"
},
{
"code": "70099003",
"display": "Stargardt's disease (disorder)"
},
{
"code": "725590001",
"display": "Butterfly-shaped pigmentary macular dystrophy (disorder)"
},
{
"code": "737273002",
"display": "Degeneration of posterior pole of eye (disorder)"
},
{
"code": "769244003",
"display": "Disorder of right macula due to diabetes mellitus (disorder)"
},
{
"code": "769245002",
"display": "Disorder of left macula due to diabetes mellitus (disorder)"
},
{
"code": "770097006",
"display": "Clinically significant macular edema due to diabetes mellitus (disorder)"
},
{
"code": "774010000",
"display": "Scarred macula of left eye (disorder)"
},
{
"code": "789220007",
"display": "Atrophy of macula lutea (disorder)"
},
{
"code": "860721006",
"display": "Disorder of macula of bilateral eyes due to diabetes mellitus (disorder)"
}
]
}
]
},
"expansion": {
"identifier": "urn:uuid:c5bf7937-e664-4e00-81c1-7b7ce3a09b54",
"timestamp": "2025-05-23T22:40:15-04:00",
"total": 118,
"contains": [
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"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "1187639002",
"display": "Martinique crinkled retinal pigment epitheliopathy (disorder)"
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{
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"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "1231253003",
"display": "Macular hole due to degenerative progressive high myopia (disorder)"
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{
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"code": "1285589003",
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{
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"code": "14046000",
"display": "Cystoid macular retinal degeneration (disorder)"
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{
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{
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"code": "15628811000119100",
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{
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"code": "15631531000119100",
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{
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"code": "15631611000119106",
"display": "Scarred macula of right eye (disorder)"
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{
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"code": "15639131000119107",
"display": "Macular edema of retina of right eye (disorder)"
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{
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{
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"code": "15639231000119102",
"display": "Macular edema of retina of bilateral eyes (disorder)"
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{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "16320791000119106",
"display": "Myopic macular degeneration of bilateral eyes (disorder)"
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{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "16320831000119100",
"display": "Myopic macular degeneration of right eye (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "16320871000119102",
"display": "Myopic macular degeneration of left eye (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "18410006",
"display": "Scarred macula (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "193350004",
"display": "Advanced maculopathy due to diabetes mellitus (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "193387007",
"display": "Cystoid macular edema (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "193410003",
"display": "Sorsby pseudoinflammatory fundus dystrophy (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "232006002",
"display": "Macular hole (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "232013002",
"display": "Macular retinoschisis (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "232014008",
"display": "Macular and peripheral retinoschisis (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "232020009",
"display": "Disorder of macula due to diabetes mellitus (disorder)"
},
{
"system": "http://snomed.info/sct",
"version": "http://snomed.info/sct/731000124108/version/20250301",
"code": "232049001",
"display": "Adult vitelliform macular dystrophy (disorder)"
},
{
"system": "http://snomed.info/sct",
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