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Packageus.nlm.vsac
Resource TypeValueSet
IdValueSet-2.16.840.1.113883.3.464.1003.120.11.1003.json
FHIR VersionR4
Sourcehttps://vsac.nlm.nih.gov/valueset/2.16.840.1.113883.3.464.1003.120.11.1003/expansion
URLhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003
Version20240206
Statusactive
Date2024-02-06T01:09:28-05:00
NameDisordersOfTheImmuneSystem
TitleDisorders of the Immune System
Realmus
Authorityhl7
Purpose(Clinical Focus: The purpose of this value set is to represent concepts for a diagnosis of conditions affecting the immune system.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of disorders of the immune system including disorders of the immunoglobulins and the complement system.),(Exclusion Criteria: No exclusions.)

Resources that use this resource

ValueSet
2.16.840.1.113883.3.464.1003.120.12.1001Disorders of the Immune System

Resources that this resource uses

CodeSystem
icd-10-cmInternational Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM)

Narrative

No narrative content found in resource


Source1

{
  "resourceType": "ValueSet",
  "id": "2.16.840.1.113883.3.464.1003.120.11.1003",
  "meta": {
    "versionId": "35",
    "lastUpdated": "2024-02-06T01:09:28.000-05:00",
    "profile": [
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  "extension": [
    {
      "url": "http://hl7.org/fhir/StructureDefinition/valueset-author",
      "valueContactDetail": {
        "name": "NCQA PHEMUR Author"
      }
    },
    {
      "url": "http://hl7.org/fhir/StructureDefinition/resource-lastReviewDate",
      "valueDate": "2025-03-10"
    },
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      "valueDate": "2024-02-06"
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  "url": "http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003",
  "identifier": [
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  ],
  "version": "20240206",
  "name": "DisordersOfTheImmuneSystem",
  "title": "Disorders of the Immune System",
  "status": "active",
  "date": "2024-02-06T01:09:28-05:00",
  "publisher": "NCQA PHEMUR",
  "jurisdiction": [
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          "system": "urn:iso:std:iso:3166",
          "code": "US"
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  "purpose": "(Clinical Focus: The purpose of this value set is to represent concepts for a diagnosis of conditions affecting the immune system.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of disorders of the immune system including disorders of the immunoglobulins and the complement system.),(Exclusion Criteria: No exclusions.)",
  "compose": {
    "include": [
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "concept": [
          {
            "code": "D80.0",
            "display": "Hereditary hypogammaglobulinemia"
          },
          {
            "code": "D80.1",
            "display": "Nonfamilial hypogammaglobulinemia"
          },
          {
            "code": "D80.2",
            "display": "Selective deficiency of immunoglobulin A [IgA]"
          },
          {
            "code": "D80.3",
            "display": "Selective deficiency of immunoglobulin G [IgG] subclasses"
          },
          {
            "code": "D80.4",
            "display": "Selective deficiency of immunoglobulin M [IgM]"
          },
          {
            "code": "D80.5",
            "display": "Immunodeficiency with increased immunoglobulin M [IgM]"
          },
          {
            "code": "D80.6",
            "display": "Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia"
          },
          {
            "code": "D80.7",
            "display": "Transient hypogammaglobulinemia of infancy"
          },
          {
            "code": "D80.8",
            "display": "Other immunodeficiencies with predominantly antibody defects"
          },
          {
            "code": "D80.9",
            "display": "Immunodeficiency with predominantly antibody defects, unspecified"
          },
          {
            "code": "D81.0",
            "display": "Severe combined immunodeficiency [SCID] with reticular dysgenesis"
          },
          {
            "code": "D81.1",
            "display": "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers"
          },
          {
            "code": "D81.2",
            "display": "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers"
          },
          {
            "code": "D81.4",
            "display": "Nezelof's syndrome"
          },
          {
            "code": "D81.6",
            "display": "Major histocompatibility complex class I deficiency"
          },
          {
            "code": "D81.7",
            "display": "Major histocompatibility complex class II deficiency"
          },
          {
            "code": "D81.82",
            "display": "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]"
          },
          {
            "code": "D81.89",
            "display": "Other combined immunodeficiencies"
          },
          {
            "code": "D81.9",
            "display": "Combined immunodeficiency, unspecified"
          },
          {
            "code": "D82.0",
            "display": "Wiskott-Aldrich syndrome"
          },
          {
            "code": "D82.1",
            "display": "Di George's syndrome"
          },
          {
            "code": "D82.2",
            "display": "Immunodeficiency with short-limbed stature"
          },
          {
            "code": "D82.3",
            "display": "Immunodeficiency following hereditary defective response to Epstein-Barr virus"
          },
          {
            "code": "D82.4",
            "display": "Hyperimmunoglobulin E [IgE] syndrome"
          },
          {
            "code": "D82.8",
            "display": "Immunodeficiency associated with other specified major defects"
          },
          {
            "code": "D82.9",
            "display": "Immunodeficiency associated with major defect, unspecified"
          },
          {
            "code": "D83.0",
            "display": "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function"
          },
          {
            "code": "D83.1",
            "display": "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders"
          },
          {
            "code": "D83.2",
            "display": "Common variable immunodeficiency with autoantibodies to B- or T-cells"
          },
          {
            "code": "D83.8",
            "display": "Other common variable immunodeficiencies"
          },
          {
            "code": "D83.9",
            "display": "Common variable immunodeficiency, unspecified"
          },
          {
            "code": "D84.0",
            "display": "Lymphocyte function antigen-1 [LFA-1] defect"
          },
          {
            "code": "D84.1",
            "display": "Defects in the complement system"
          },
          {
            "code": "D84.81",
            "display": "Immunodeficiency due to conditions classified elsewhere"
          },
          {
            "code": "D84.821",
            "display": "Immunodeficiency due to drugs"
          },
          {
            "code": "D84.822",
            "display": "Immunodeficiency due to external causes"
          },
          {
            "code": "D84.89",
            "display": "Other immunodeficiencies"
          },
          {
            "code": "D84.9",
            "display": "Immunodeficiency, unspecified"
          },
          {
            "code": "D89.3",
            "display": "Immune reconstitution syndrome"
          },
          {
            "code": "D89.810",
            "display": "Acute graft-versus-host disease"
          },
          {
            "code": "D89.811",
            "display": "Chronic graft-versus-host disease"
          },
          {
            "code": "D89.812",
            "display": "Acute on chronic graft-versus-host disease"
          },
          {
            "code": "D89.813",
            "display": "Graft-versus-host disease, unspecified"
          },
          {
            "code": "D89.82",
            "display": "Autoimmune lymphoproliferative syndrome [ALPS]"
          },
          {
            "code": "D89.831",
            "display": "Cytokine release syndrome, grade 1"
          },
          {
            "code": "D89.832",
            "display": "Cytokine release syndrome, grade 2"
          },
          {
            "code": "D89.833",
            "display": "Cytokine release syndrome, grade 3"
          },
          {
            "code": "D89.834",
            "display": "Cytokine release syndrome, grade 4"
          },
          {
            "code": "D89.835",
            "display": "Cytokine release syndrome, grade 5"
          },
          {
            "code": "D89.839",
            "display": "Cytokine release syndrome, grade unspecified"
          },
          {
            "code": "D89.84",
            "display": "IgG4-related disease"
          },
          {
            "code": "D89.89",
            "display": "Other specified disorders involving the immune mechanism, not elsewhere classified"
          },
          {
            "code": "D89.9",
            "display": "Disorder involving the immune mechanism, unspecified"
          }
        ]
      }
    ]
  },
  "expansion": {
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    "timestamp": "2025-05-23T22:27:22-04:00",
    "total": 53,
    "contains": [
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.0",
        "display": "Hereditary hypogammaglobulinemia"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.1",
        "display": "Nonfamilial hypogammaglobulinemia"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.2",
        "display": "Selective deficiency of immunoglobulin A [IgA]"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.3",
        "display": "Selective deficiency of immunoglobulin G [IgG] subclasses"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.4",
        "display": "Selective deficiency of immunoglobulin M [IgM]"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.5",
        "display": "Immunodeficiency with increased immunoglobulin M [IgM]"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.6",
        "display": "Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.7",
        "display": "Transient hypogammaglobulinemia of infancy"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.8",
        "display": "Other immunodeficiencies with predominantly antibody defects"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D80.9",
        "display": "Immunodeficiency with predominantly antibody defects, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.0",
        "display": "Severe combined immunodeficiency [SCID] with reticular dysgenesis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.1",
        "display": "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.2",
        "display": "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.4",
        "display": "Nezelof's syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.6",
        "display": "Major histocompatibility complex class I deficiency"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.7",
        "display": "Major histocompatibility complex class II deficiency"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.82",
        "display": "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.89",
        "display": "Other combined immunodeficiencies"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D81.9",
        "display": "Combined immunodeficiency, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.0",
        "display": "Wiskott-Aldrich syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.1",
        "display": "Di George's syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.2",
        "display": "Immunodeficiency with short-limbed stature"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.3",
        "display": "Immunodeficiency following hereditary defective response to Epstein-Barr virus"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.4",
        "display": "Hyperimmunoglobulin E [IgE] syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.8",
        "display": "Immunodeficiency associated with other specified major defects"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D82.9",
        "display": "Immunodeficiency associated with major defect, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D83.0",
        "display": "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D83.1",
        "display": "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D83.2",
        "display": "Common variable immunodeficiency with autoantibodies to B- or T-cells"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D83.8",
        "display": "Other common variable immunodeficiencies"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D83.9",
        "display": "Common variable immunodeficiency, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.0",
        "display": "Lymphocyte function antigen-1 [LFA-1] defect"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.1",
        "display": "Defects in the complement system"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.81",
        "display": "Immunodeficiency due to conditions classified elsewhere"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.821",
        "display": "Immunodeficiency due to drugs"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.822",
        "display": "Immunodeficiency due to external causes"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.89",
        "display": "Other immunodeficiencies"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D84.9",
        "display": "Immunodeficiency, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.3",
        "display": "Immune reconstitution syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.810",
        "display": "Acute graft-versus-host disease"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.811",
        "display": "Chronic graft-versus-host disease"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.812",
        "display": "Acute on chronic graft-versus-host disease"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.813",
        "display": "Graft-versus-host disease, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.82",
        "display": "Autoimmune lymphoproliferative syndrome [ALPS]"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.831",
        "display": "Cytokine release syndrome, grade 1"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.832",
        "display": "Cytokine release syndrome, grade 2"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.833",
        "display": "Cytokine release syndrome, grade 3"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.834",
        "display": "Cytokine release syndrome, grade 4"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.835",
        "display": "Cytokine release syndrome, grade 5"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.839",
        "display": "Cytokine release syndrome, grade unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.84",
        "display": "IgG4-related disease"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.89",
        "display": "Other specified disorders involving the immune mechanism, not elsewhere classified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2025",
        "code": "D89.9",
        "display": "Disorder involving the immune mechanism, unspecified"
      }
    ]
  }
}