FHIR IG analytics
| Package | us.nlm.vsac |
| Resource Type | ValueSet |
| Id | ValueSet-2.16.840.1.113883.3.464.1003.120.11.1003.json |
| FHIR Version | R4 |
| Source | https://vsac.nlm.nih.gov/valueset/2.16.840.1.113883.3.464.1003.120.11.1003/expansion |
| URL | http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003 |
| Version | 20240206 |
| Status | active |
| Date | 2024-02-06T01:09:28-05:00 |
| Name | DisordersOfTheImmuneSystem |
| Title | Disorders of the Immune System |
| Realm | us |
| Authority | hl7 |
| Purpose | (Clinical Focus: The purpose of this value set is to represent concepts for a diagnosis of conditions affecting the immune system.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of disorders of the immune system including disorders of the immunoglobulins and the complement system.),(Exclusion Criteria: No exclusions.) |
Resources that use this resource
Resources that this resource uses
| CodeSystem |
| icd-10-cm | International Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM) |
Narrative
No narrative content found in resource
Source1
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"title": "Disorders of the Immune System",
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"date": "2024-02-06T01:09:28-05:00",
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{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"concept": [
{
"code": "D80.0",
"display": "Hereditary hypogammaglobulinemia"
},
{
"code": "D80.1",
"display": "Nonfamilial hypogammaglobulinemia"
},
{
"code": "D80.2",
"display": "Selective deficiency of immunoglobulin A [IgA]"
},
{
"code": "D80.3",
"display": "Selective deficiency of immunoglobulin G [IgG] subclasses"
},
{
"code": "D80.4",
"display": "Selective deficiency of immunoglobulin M [IgM]"
},
{
"code": "D80.5",
"display": "Immunodeficiency with increased immunoglobulin M [IgM]"
},
{
"code": "D80.6",
"display": "Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia"
},
{
"code": "D80.7",
"display": "Transient hypogammaglobulinemia of infancy"
},
{
"code": "D80.8",
"display": "Other immunodeficiencies with predominantly antibody defects"
},
{
"code": "D80.9",
"display": "Immunodeficiency with predominantly antibody defects, unspecified"
},
{
"code": "D81.0",
"display": "Severe combined immunodeficiency [SCID] with reticular dysgenesis"
},
{
"code": "D81.1",
"display": "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers"
},
{
"code": "D81.2",
"display": "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers"
},
{
"code": "D81.4",
"display": "Nezelof's syndrome"
},
{
"code": "D81.6",
"display": "Major histocompatibility complex class I deficiency"
},
{
"code": "D81.7",
"display": "Major histocompatibility complex class II deficiency"
},
{
"code": "D81.82",
"display": "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]"
},
{
"code": "D81.89",
"display": "Other combined immunodeficiencies"
},
{
"code": "D81.9",
"display": "Combined immunodeficiency, unspecified"
},
{
"code": "D82.0",
"display": "Wiskott-Aldrich syndrome"
},
{
"code": "D82.1",
"display": "Di George's syndrome"
},
{
"code": "D82.2",
"display": "Immunodeficiency with short-limbed stature"
},
{
"code": "D82.3",
"display": "Immunodeficiency following hereditary defective response to Epstein-Barr virus"
},
{
"code": "D82.4",
"display": "Hyperimmunoglobulin E [IgE] syndrome"
},
{
"code": "D82.8",
"display": "Immunodeficiency associated with other specified major defects"
},
{
"code": "D82.9",
"display": "Immunodeficiency associated with major defect, unspecified"
},
{
"code": "D83.0",
"display": "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function"
},
{
"code": "D83.1",
"display": "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders"
},
{
"code": "D83.2",
"display": "Common variable immunodeficiency with autoantibodies to B- or T-cells"
},
{
"code": "D83.8",
"display": "Other common variable immunodeficiencies"
},
{
"code": "D83.9",
"display": "Common variable immunodeficiency, unspecified"
},
{
"code": "D84.0",
"display": "Lymphocyte function antigen-1 [LFA-1] defect"
},
{
"code": "D84.1",
"display": "Defects in the complement system"
},
{
"code": "D84.81",
"display": "Immunodeficiency due to conditions classified elsewhere"
},
{
"code": "D84.821",
"display": "Immunodeficiency due to drugs"
},
{
"code": "D84.822",
"display": "Immunodeficiency due to external causes"
},
{
"code": "D84.89",
"display": "Other immunodeficiencies"
},
{
"code": "D84.9",
"display": "Immunodeficiency, unspecified"
},
{
"code": "D89.3",
"display": "Immune reconstitution syndrome"
},
{
"code": "D89.810",
"display": "Acute graft-versus-host disease"
},
{
"code": "D89.811",
"display": "Chronic graft-versus-host disease"
},
{
"code": "D89.812",
"display": "Acute on chronic graft-versus-host disease"
},
{
"code": "D89.813",
"display": "Graft-versus-host disease, unspecified"
},
{
"code": "D89.82",
"display": "Autoimmune lymphoproliferative syndrome [ALPS]"
},
{
"code": "D89.831",
"display": "Cytokine release syndrome, grade 1"
},
{
"code": "D89.832",
"display": "Cytokine release syndrome, grade 2"
},
{
"code": "D89.833",
"display": "Cytokine release syndrome, grade 3"
},
{
"code": "D89.834",
"display": "Cytokine release syndrome, grade 4"
},
{
"code": "D89.835",
"display": "Cytokine release syndrome, grade 5"
},
{
"code": "D89.839",
"display": "Cytokine release syndrome, grade unspecified"
},
{
"code": "D89.84",
"display": "IgG4-related disease"
},
{
"code": "D89.89",
"display": "Other specified disorders involving the immune mechanism, not elsewhere classified"
},
{
"code": "D89.9",
"display": "Disorder involving the immune mechanism, unspecified"
}
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}
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"timestamp": "2025-05-23T22:27:22-04:00",
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.0",
"display": "Hereditary hypogammaglobulinemia"
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.1",
"display": "Nonfamilial hypogammaglobulinemia"
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.2",
"display": "Selective deficiency of immunoglobulin A [IgA]"
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.3",
"display": "Selective deficiency of immunoglobulin G [IgG] subclasses"
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.4",
"display": "Selective deficiency of immunoglobulin M [IgM]"
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.5",
"display": "Immunodeficiency with increased immunoglobulin M [IgM]"
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
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"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.7",
"display": "Transient hypogammaglobulinemia of infancy"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.8",
"display": "Other immunodeficiencies with predominantly antibody defects"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D80.9",
"display": "Immunodeficiency with predominantly antibody defects, unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.0",
"display": "Severe combined immunodeficiency [SCID] with reticular dysgenesis"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.1",
"display": "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.2",
"display": "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.4",
"display": "Nezelof's syndrome"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.6",
"display": "Major histocompatibility complex class I deficiency"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.7",
"display": "Major histocompatibility complex class II deficiency"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.82",
"display": "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.89",
"display": "Other combined immunodeficiencies"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D81.9",
"display": "Combined immunodeficiency, unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.0",
"display": "Wiskott-Aldrich syndrome"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.1",
"display": "Di George's syndrome"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.2",
"display": "Immunodeficiency with short-limbed stature"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.3",
"display": "Immunodeficiency following hereditary defective response to Epstein-Barr virus"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.4",
"display": "Hyperimmunoglobulin E [IgE] syndrome"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.8",
"display": "Immunodeficiency associated with other specified major defects"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D82.9",
"display": "Immunodeficiency associated with major defect, unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D83.0",
"display": "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D83.1",
"display": "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D83.2",
"display": "Common variable immunodeficiency with autoantibodies to B- or T-cells"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D83.8",
"display": "Other common variable immunodeficiencies"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D83.9",
"display": "Common variable immunodeficiency, unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.0",
"display": "Lymphocyte function antigen-1 [LFA-1] defect"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.1",
"display": "Defects in the complement system"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.81",
"display": "Immunodeficiency due to conditions classified elsewhere"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.821",
"display": "Immunodeficiency due to drugs"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.822",
"display": "Immunodeficiency due to external causes"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.89",
"display": "Other immunodeficiencies"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D84.9",
"display": "Immunodeficiency, unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.3",
"display": "Immune reconstitution syndrome"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.810",
"display": "Acute graft-versus-host disease"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.811",
"display": "Chronic graft-versus-host disease"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.812",
"display": "Acute on chronic graft-versus-host disease"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.813",
"display": "Graft-versus-host disease, unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.82",
"display": "Autoimmune lymphoproliferative syndrome [ALPS]"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.831",
"display": "Cytokine release syndrome, grade 1"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.832",
"display": "Cytokine release syndrome, grade 2"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.833",
"display": "Cytokine release syndrome, grade 3"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.834",
"display": "Cytokine release syndrome, grade 4"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.835",
"display": "Cytokine release syndrome, grade 5"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.839",
"display": "Cytokine release syndrome, grade unspecified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.84",
"display": "IgG4-related disease"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.89",
"display": "Other specified disorders involving the immune mechanism, not elsewhere classified"
},
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"version": "2025",
"code": "D89.9",
"display": "Disorder involving the immune mechanism, unspecified"
}
]
}
}