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Packageus.nlm.vsac
Resource TypeValueSet
IdValueSet-2.16.840.1.113762.1.4.1146.2996.json
FHIR VersionR4
Sourcehttps://vsac.nlm.nih.gov/valueset/2.16.840.1.113762.1.4.1146.2996/expansion
URLhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113762.1.4.1146.2996
Version20251010
Statusactive
Date2025-10-10T01:04:17-04:00
NameNephroticSyndromeSNOMED
TitleNephrotic Syndrome (SNOMED)
Realmus
Authorityhl7
Purpose(Clinical Focus: This set of values contains diagnoses or problems that represent that the patient has Nephrotic Syndrome regardless of the clinical presentation of the condition),(Data Element Scope: Diagnoses or problems documented in a clinical record),(Inclusion Criteria: Nephrotic Syndrome),(Exclusion Criteria: None)

Resources that use this resource

No resources found


Resources that this resource uses

CodeSystem
sctSNOMED codes used in this IG

Narrative

No narrative content found in resource


Source1

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  "meta": {
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  ],
  "version": "20251010",
  "name": "NephroticSyndromeSNOMED",
  "title": "Nephrotic Syndrome (SNOMED)",
  "status": "active",
  "date": "2025-10-10T01:04:17-04:00",
  "publisher": "CSTE Steward",
  "jurisdiction": [
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      "coding": [
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          "system": "urn:iso:std:iso:3166",
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        }
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  "compose": {
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        "concept": [
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            "code": "1081801000112104",
            "display": "Acute nephrotic syndrome (disorder)"
          },
          {
            "code": "1187040004",
            "display": "Familial steroid-resistant nephrotic syndrome with adrenal insufficiency (disorder)"
          },
          {
            "code": "1260194003",
            "display": "Idiopathic steroid-resistant nephrotic syndrome (disorder)"
          },
          {
            "code": "1260198000",
            "display": "Idiopathic steroid-sensitive nephrotic syndrome with secondary steroid resistance (disorder)"
          },
          {
            "code": "197589005",
            "display": "Nephrotic syndrome with proliferative glomerulonephritis (disorder)"
          },
          {
            "code": "197590001",
            "display": "Nephrotic syndrome with membranous glomerulonephritis (disorder)"
          },
          {
            "code": "197591002",
            "display": "Nephrotic syndrome with membranoproliferative glomerulonephritis (disorder)"
          },
          {
            "code": "197593004",
            "display": "Nephrotic syndrome, minor glomerular abnormality (disorder)"
          },
          {
            "code": "197594005",
            "display": "Nephrotic syndrome, focal and segmental glomerular lesions (disorder)"
          },
          {
            "code": "197595006",
            "display": "Nephrotic syndrome, diffuse membranous glomerulonephritis (disorder)"
          },
          {
            "code": "197596007",
            "display": "Nephrotic syndrome, diffuse mesangial proliferative glomerulonephritis (disorder)"
          },
          {
            "code": "197597003",
            "display": "Nephrotic syndrome, diffuse endocapillary proliferative glomerulonephritis (disorder)"
          },
          {
            "code": "197598008",
            "display": "Nephrotic syndrome, diffuse mesangiocapillary glomerulonephritis (disorder)"
          },
          {
            "code": "197599000",
            "display": "Nephrotic syndrome, dense deposit disease (disorder)"
          },
          {
            "code": "197600002",
            "display": "Nephrotic syndrome, diffuse crescentic glomerulonephritis (disorder)"
          },
          {
            "code": "197601003",
            "display": "Finnish congenital nephrotic syndrome (disorder)"
          },
          {
            "code": "197604006",
            "display": "Nephrotic syndrome in amyloidosis (disorder)"
          },
          {
            "code": "197606008",
            "display": "Nephrotic syndrome in malaria (disorder)"
          },
          {
            "code": "197607004",
            "display": "Nephrotic syndrome in polyarteritis nodosa (disorder)"
          },
          {
            "code": "236380004",
            "display": "Steroid-sensitive nephrotic syndrome (disorder)"
          },
          {
            "code": "236381000",
            "display": "Steroid-resistant nephrotic syndrome (disorder)"
          },
          {
            "code": "236382007",
            "display": "Steroid-dependent nephrotic syndrome (disorder)"
          },
          {
            "code": "236384008",
            "display": "Congenital nephrotic syndrome with focal glomerulosclerosis (disorder)"
          },
          {
            "code": "363233007",
            "display": "Nephrotic syndrome secondary to glomerulonephritis (disorder)"
          },
          {
            "code": "363234001",
            "display": "Nephrotic syndrome secondary to systemic disease (disorder)"
          },
          {
            "code": "445119005",
            "display": "Steroid sensitive nephrotic syndrome of childhood (disorder)"
          },
          {
            "code": "449820008",
            "display": "Steroid resistant nephrotic syndrome of childhood (disorder)"
          },
          {
            "code": "48796009",
            "display": "Congenital nephrotic syndrome (disorder)"
          },
          {
            "code": "52254009",
            "display": "Nephrotic syndrome (disorder)"
          },
          {
            "code": "705065000",
            "display": "Childhood nephrotic syndrome (disorder)"
          },
          {
            "code": "713695001",
            "display": "Nephrotic syndrome co-occurrent with human immunodeficiency virus infection (disorder)"
          },
          {
            "code": "717191005",
            "display": "Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)"
          },
          {
            "code": "717760006",
            "display": "Multi-drug resistant nephrotic syndrome (disorder)"
          },
          {
            "code": "718141008",
            "display": "Genetic steroid-resistant nephrotic syndrome (disorder)"
          },
          {
            "code": "733453005",
            "display": "Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome (disorder)"
          },
          {
            "code": "771447009",
            "display": "Laminin subunit beta 2 related infantile-onset nephrotic syndrome (disorder)"
          },
          {
            "code": "773647007",
            "display": "Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome (disorder)"
          },
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            "code": "783614008",
            "display": "Familial steroid-resistant nephrotic syndrome with sensorineural deafness (disorder)"
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    "timestamp": "2025-11-24T13:49:28-05:00",
    "total": 38,
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        "system": "http://snomed.info/sct",
        "version": "http://snomed.info/sct/731000124108/version/20250901",
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        "system": "http://snomed.info/sct",
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        "system": "http://snomed.info/sct",
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        "display": "Nephrotic syndrome in amyloidosis (disorder)"
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        "version": "http://snomed.info/sct/731000124108/version/20250901",
        "code": "236384008",
        "display": "Congenital nephrotic syndrome with focal glomerulosclerosis (disorder)"
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        "code": "449820008",
        "display": "Steroid resistant nephrotic syndrome of childhood (disorder)"
      },
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      {
        "system": "http://snomed.info/sct",
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        "version": "http://snomed.info/sct/731000124108/version/20250901",
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        "display": "Laminin subunit beta 2 related infantile-onset nephrotic syndrome (disorder)"
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        "system": "http://snomed.info/sct",
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}