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Packageus.nlm.vsac
Resource TypeValueSet
IdValueSet-2.16.840.1.113762.1.4.1146.2995.json
FHIR VersionR4
Sourcehttps://vsac.nlm.nih.gov/valueset/2.16.840.1.113762.1.4.1146.2995/expansion
URLhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113762.1.4.1146.2995
Version20251010
Statusactive
Date2025-10-10T01:04:17-04:00
NameNephroticSyndromeICD10CM
TitleNephrotic Syndrome (ICD10CM)
Realmus
Authorityhl7
Purpose(Clinical Focus: This set of values contains diagnoses or problems that represent that the patient has Nephrotic Syndrome regardless of the clinical presentation of the condition),(Data Element Scope: Diagnoses or problems documented in a clinical record),(Inclusion Criteria: Nephrotic Syndrome),(Exclusion Criteria: None)

Resources that use this resource

No resources found


Resources that this resource uses

CodeSystem
icd-10-cmInternational Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM)

Narrative

No narrative content found in resource


Source1

{
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  "meta": {
    "versionId": "6",
    "lastUpdated": "2025-10-10T01:04:17.000-04:00",
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  },
  "extension": [
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      "valueContactDetail": {
        "name": "CSTE Author"
      }
    },
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      "valueString": "TES"
    },
    {
      "url": "http://hl7.org/fhir/StructureDefinition/resource-lastReviewDate",
      "valueDate": "2025-10-10"
    },
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  "url": "http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113762.1.4.1146.2995",
  "identifier": [
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      "system": "urn:ietf:rfc:3986",
      "value": "urn:oid:2.16.840.1.113762.1.4.1146.2995"
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  ],
  "version": "20251010",
  "name": "NephroticSyndromeICD10CM",
  "title": "Nephrotic Syndrome (ICD10CM)",
  "status": "active",
  "date": "2025-10-10T01:04:17-04:00",
  "publisher": "CSTE Steward",
  "jurisdiction": [
    {
      "coding": [
        {
          "system": "urn:iso:std:iso:3166",
          "code": "US"
        }
      ]
    }
  ],
  "purpose": "(Clinical Focus: This set of values contains diagnoses or problems that represent that the patient has Nephrotic Syndrome regardless of the clinical presentation of the condition),(Data Element Scope: Diagnoses or problems documented in a clinical record),(Inclusion Criteria: Nephrotic Syndrome),(Exclusion Criteria: None)",
  "compose": {
    "include": [
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "concept": [
          {
            "code": "N04.0",
            "display": "Nephrotic syndrome with minor glomerular abnormality"
          },
          {
            "code": "N04.1",
            "display": "Nephrotic syndrome with focal and segmental glomerular lesions"
          },
          {
            "code": "N04.20",
            "display": "Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified"
          },
          {
            "code": "N04.21",
            "display": "Primary membranous nephropathy with nephrotic syndrome"
          },
          {
            "code": "N04.22",
            "display": "Secondary membranous nephropathy with nephrotic syndrome"
          },
          {
            "code": "N04.29",
            "display": "Other nephrotic syndrome with diffuse membranous glomerulonephritis"
          },
          {
            "code": "N04.3",
            "display": "Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis"
          },
          {
            "code": "N04.4",
            "display": "Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis"
          },
          {
            "code": "N04.5",
            "display": "Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis"
          },
          {
            "code": "N04.6",
            "display": "Nephrotic syndrome with dense deposit disease"
          },
          {
            "code": "N04.7",
            "display": "Nephrotic syndrome with diffuse crescentic glomerulonephritis"
          },
          {
            "code": "N04.8",
            "display": "Nephrotic syndrome with other morphologic changes"
          },
          {
            "code": "N04.9",
            "display": "Nephrotic syndrome with unspecified morphologic changes"
          },
          {
            "code": "N04.A",
            "display": "Nephrotic syndrome with C3 glomerulonephritis"
          },
          {
            "code": "N04.B1",
            "display": "Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)"
          },
          {
            "code": "N04.B2",
            "display": "Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)"
          },
          {
            "code": "Z87.441",
            "display": "Personal history of nephrotic syndrome"
          }
        ]
      }
    ]
  },
  "expansion": {
    "identifier": "urn:uuid:b63181e5-b671-44f0-8fcc-a591f00e5281",
    "timestamp": "2025-11-24T13:49:25-05:00",
    "total": 17,
    "contains": [
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.0",
        "display": "Nephrotic syndrome with minor glomerular abnormality"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.1",
        "display": "Nephrotic syndrome with focal and segmental glomerular lesions"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.20",
        "display": "Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.21",
        "display": "Primary membranous nephropathy with nephrotic syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.22",
        "display": "Secondary membranous nephropathy with nephrotic syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.29",
        "display": "Other nephrotic syndrome with diffuse membranous glomerulonephritis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.3",
        "display": "Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.4",
        "display": "Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.5",
        "display": "Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.6",
        "display": "Nephrotic syndrome with dense deposit disease"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.7",
        "display": "Nephrotic syndrome with diffuse crescentic glomerulonephritis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.8",
        "display": "Nephrotic syndrome with other morphologic changes"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.9",
        "display": "Nephrotic syndrome with unspecified morphologic changes"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.A",
        "display": "Nephrotic syndrome with C3 glomerulonephritis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.B1",
        "display": "Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "N04.B2",
        "display": "Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "version": "2026",
        "code": "Z87.441",
        "display": "Personal history of nephrotic syndrome"
      }
    ]
  }
}