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FHIR IG Statistics: ValueSet/2.16.840.1.113883.3.526.2.1646

Packageus.nlm.vsac
Resource TypeValueSet
Id2.16.840.1.113883.3.526.2.1646
FHIR VersionR4
Sourcehttp://fhir.org/packages/us.nlm.vsac/https://vsac.nlm.nih.gov/valueset/2.16.840.1.113883.3.526.2.1646/expansion
URLhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.526.2.1646
Version20250125
Statusactive
Date2025-01-25T01:09:35-05:00
NameDegenerativeDisordersOfGlobe
TitleDegenerative Disorders of Globe
Realmus
Authorityhl7
Purpose(Clinical Focus: The purpose of this value set is to represent concepts of a diagnosis of degenerative disorders of globe.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of degenerative disorders of globe, including degenerative myopia, chalcosis, siderosis, and other degenerative diagnoses.),(Exclusion Criteria: Excludes concepts that represent a diagnosis for 'unspecified eye.')

Resources that use this resource

ValueSet
2.16.840.1.113883.3.526.3.1454Degenerative Disorders of Globe

Resources that this resource uses

CodeSystem
sctSNOMED CT (all versions)

Narrative

No narrative content found in resource


Source

{
  "resourceType": "ValueSet",
  "id": "2.16.840.1.113883.3.526.2.1646",
  "meta": {
    "versionId": "43",
    "lastUpdated": "2025-01-25T01:09:35.000-05:00",
    "profile": [
      "http://hl7.org/fhir/StructureDefinition/shareablevalueset",
      "http://hl7.org/fhir/us/cqfmeasures/StructureDefinition/computable-valueset-cqfm",
      "http://hl7.org/fhir/us/cqfmeasures/StructureDefinition/publishable-valueset-cqfm"
    ]
  },
  "extension": [
    {
      "url": "http://hl7.org/fhir/StructureDefinition/valueset-author",
      "valueContactDetail": {
        "name": "American Academy of Ophthalmology Author"
      }
    },
    {
      "url": "http://hl7.org/fhir/StructureDefinition/resource-lastReviewDate",
      "valueDate": "2025-05-12"
    },
    {
      "url": "http://hl7.org/fhir/StructureDefinition/valueset-effectiveDate",
      "valueDate": "2025-01-25"
    }
  ],
  "url": "http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.526.2.1646",
  "identifier": [
    {
      "system": "urn:ietf:rfc:3986",
      "value": "urn:oid:2.16.840.1.113883.3.526.2.1646"
    }
  ],
  "version": "20250125",
  "name": "DegenerativeDisordersOfGlobe",
  "title": "Degenerative Disorders of Globe",
  "status": "active",
  "date": "2025-01-25T01:09:35-05:00",
  "publisher": "American Academy of Ophthalmology Steward",
  "jurisdiction": [
    {
      "coding": [
        {
          "system": "urn:iso:std:iso:3166",
          "code": "US"
        }
      ]
    }
  ],
  "purpose": "(Clinical Focus: The purpose of this value set is to represent concepts of a diagnosis of degenerative disorders of globe.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of degenerative disorders of globe, including degenerative myopia, chalcosis, siderosis, and other degenerative diagnoses.),(Exclusion Criteria: Excludes concepts that represent a diagnosis for 'unspecified eye.')",
  "compose": {
    "include": [
      {
        "system": "http://snomed.info/sct",
        "concept": [
          {
            "code": "111521006",
            "display": "Corneal degeneration (disorder)"
          },
          {
            "code": "1208890001",
            "display": "Advanced exudative age related macular degeneration (disorder)"
          },
          {
            "code": "1208895006",
            "display": "Advanced age related macular degeneration (disorder)"
          },
          {
            "code": "1285507004",
            "display": "Nonexudative neovascular age-related macular degeneration (disorder)"
          },
          {
            "code": "1285555004",
            "display": "Peripheral exudative hemorrhagic chorioretinopathy (disorder)"
          },
          {
            "code": "1296526000",
            "display": "Disciform macular degeneration (disorder)"
          },
          {
            "code": "14046000",
            "display": "Cystoid macular retinal degeneration (disorder)"
          },
          {
            "code": "15628651000119100",
            "display": "Sorsby pseudoinflammatory fundus dystrophy of right eye (disorder)"
          },
          {
            "code": "15628691000119105",
            "display": "Sorsby pseudoinflammatory fundus dystrophy of left eye (disorder)"
          },
          {
            "code": "15628731000119103",
            "display": "Sorsby pseudoinflammatory fundus dystrophy of bilateral eyes (disorder)"
          },
          {
            "code": "15632931000119101",
            "display": "Bilateral age-related nonexudative macular degeneration (disorder)"
          },
          {
            "code": "15632971000119103",
            "display": "Age-related nonexudative macular degeneration of left eye (disorder)"
          },
          {
            "code": "15633011000119103",
            "display": "Age-related nonexudative macular degeneration of right eye (disorder)"
          },
          {
            "code": "15633051000119102",
            "display": "Age-related exudative macular degeneration of right eye (disorder)"
          },
          {
            "code": "15633091000119107",
            "display": "Age-related exudative macular degeneration of left eye (disorder)"
          },
          {
            "code": "15732881000119102",
            "display": "Generalized degeneration of retina of bilateral eyes (disorder)"
          },
          {
            "code": "15732921000119109",
            "display": "Generalized degeneration of retina of left eye (disorder)"
          },
          {
            "code": "15732961000119104",
            "display": "Generalized degeneration of retina of right eye (disorder)"
          },
          {
            "code": "15733361000119105",
            "display": "Peripheral retinal degeneration of left eye (disorder)"
          },
          {
            "code": "15733401000119101",
            "display": "Peripheral retinal degeneration of right eye (disorder)"
          },
          {
            "code": "15735721000119100",
            "display": "Degeneration of cornea of left eye (disorder)"
          },
          {
            "code": "15735801000119102",
            "display": "Degeneration of cornea of bilateral eyes (disorder)"
          },
          {
            "code": "16419701000119108",
            "display": "Vitreoretinal tuft of bilateral eyes (disorder)"
          },
          {
            "code": "16419741000119105",
            "display": "Vitreoretinal tuft of right eye (disorder)"
          },
          {
            "code": "16419781000119100",
            "display": "Vitreoretinal tuft of left eye (disorder)"
          },
          {
            "code": "193410003",
            "display": "Sorsby pseudoinflammatory fundus dystrophy (disorder)"
          },
          {
            "code": "193508003",
            "display": "Ciliary body degenerative changes (disorder)"
          },
          {
            "code": "231918006",
            "display": "Chalcosis of cornea (disorder)"
          },
          {
            "code": "231919003",
            "display": "Siderosis of cornea (disorder)"
          },
          {
            "code": "231927007",
            "display": "Fatty degeneration of cornea (disorder)"
          },
          {
            "code": "231929005",
            "display": "Corneal epithelial degeneration (disorder)"
          },
          {
            "code": "231944006",
            "display": "Labrador keratopathy (disorder)"
          },
          {
            "code": "232001007",
            "display": "Snail-track retinal degeneration (disorder)"
          },
          {
            "code": "232002000",
            "display": "Snowflake retinal degeneration (disorder)"
          },
          {
            "code": "232065000",
            "display": "Goldmann-Favre syndrome (disorder)"
          },
          {
            "code": "232076001",
            "display": "Amyloid of vitreous (disorder)"
          },
          {
            "code": "24210004",
            "display": "Congenital chorioretinal degeneration (disorder)"
          },
          {
            "code": "246877005",
            "display": "Bulbar conjunctival degeneration (disorder)"
          },
          {
            "code": "246937001",
            "display": "Microcystoid epithelial degeneration of cornea (disorder)"
          },
          {
            "code": "247177004",
            "display": "Chorioretinal degeneration (disorder)"
          },
          {
            "code": "247182006",
            "display": "Vitreoretinal degeneration (disorder)"
          },
          {
            "code": "247183001",
            "display": "Peripheral snowflake retinal degeneration (disorder)"
          },
          {
            "code": "25277000",
            "display": "Siderosis of eye (disorder)"
          },
          {
            "code": "264008",
            "display": "Blind hypertensive eye (disorder)"
          },
          {
            "code": "264633009",
            "display": "Drusen stage macular degeneration (disorder)"
          },
          {
            "code": "267612009",
            "display": "Degeneration of macula due to cyst, hole or pseudohole (disorder)"
          },
          {
            "code": "267718000",
            "display": "Age-related macular degeneration (disorder)"
          },
          {
            "code": "27971006",
            "display": "Terrien's marginal degeneration of cornea (disorder)"
          },
          {
            "code": "28143002",
            "display": "Phthisical cornea (disorder)"
          },
          {
            "code": "314010006",
            "display": "Diffuse exudative maculopathy due to diabetes mellitus (disorder)"
          },
          {
            "code": "314427006",
            "display": "Drusen plus pigment change stage macular degeneration (disorder)"
          },
          {
            "code": "331381000119100",
            "display": "Vitreous degeneration of right eye (disorder)"
          },
          {
            "code": "332441000119107",
            "display": "Paving stone retinal degeneration of right eye (disorder)"
          },
          {
            "code": "332481000119102",
            "display": "Lattice degeneration of right retina (disorder)"
          },
          {
            "code": "333241000119103",
            "display": "Degeneration of peripheral cornea of right eye (disorder)"
          },
          {
            "code": "333591000119109",
            "display": "Siderosis of right eye (disorder)"
          },
          {
            "code": "333661000119101",
            "display": "Nodular degeneration of right cornea (disorder)"
          },
          {
            "code": "335531000119109",
            "display": "Cystoid macular degeneration of right retina (disorder)"
          },
          {
            "code": "335881000119108",
            "display": "Degeneration of ciliary body of right eye (disorder)"
          },
          {
            "code": "336991000119108",
            "display": "Vitreous degeneration of left eye (disorder)"
          },
          {
            "code": "338051000119103",
            "display": "Paving stone retinal degeneration of left eye (disorder)"
          },
          {
            "code": "338091000119108",
            "display": "Lattice degeneration of left retina (disorder)"
          },
          {
            "code": "338851000119105",
            "display": "Degeneration of peripheral cornea of left eye (disorder)"
          },
          {
            "code": "339201000119102",
            "display": "Siderosis of left eye (disorder)"
          },
          {
            "code": "339261000119101",
            "display": "Nodular degeneration of left cornea (disorder)"
          },
          {
            "code": "341141000119106",
            "display": "Cystoid macular degeneration of left retina (disorder)"
          },
          {
            "code": "341491000119105",
            "display": "Degeneration of ciliary body of left eye (disorder)"
          },
          {
            "code": "343101000119108",
            "display": "Vitreous degeneration of bilateral eyes (disorder)"
          },
          {
            "code": "343821000119109",
            "display": "Paving stone retinal degeneration of bilateral eyes (disorder)"
          },
          {
            "code": "343841000119103",
            "display": "Microcystoid retinal degeneration of bilateral eyes (disorder)"
          },
          {
            "code": "343861000119104",
            "display": "Lattice degeneration of bilateral retinas (disorder)"
          },
          {
            "code": "344621000119108",
            "display": "Degeneration of peripheral cornea of bilateral eyes (disorder)"
          },
          {
            "code": "344951000119107",
            "display": "Siderosis of bilateral eyes (disorder)"
          },
          {
            "code": "345021000119104",
            "display": "Nodular degeneration of bilateral corneas (disorder)"
          },
          {
            "code": "346401000119108",
            "display": "Cystoid macular degeneration of bilateral retinas (disorder)"
          },
          {
            "code": "346741000119102",
            "display": "Degeneration of ciliary body of bilateral eyes (disorder)"
          },
          {
            "code": "347251000119109",
            "display": "Senile reticular retinal degeneration of bilateral eyes (disorder)"
          },
          {
            "code": "348071000119106",
            "display": "Posterior vitreous degeneration of right eye (disorder)"
          },
          {
            "code": "348521000119104",
            "display": "Posterior vitreous degeneration of left eye (disorder)"
          },
          {
            "code": "349111000119108",
            "display": "Posterior vitreous degeneration of bilateral eyes (disorder)"
          },
          {
            "code": "35545005",
            "display": "Secondary pigmentary retinal degeneration (disorder)"
          },
          {
            "code": "3577000",
            "display": "Retinal lattice degeneration (disorder)"
          },
          {
            "code": "36524008",
            "display": "Hyaline dystrophy of Bruch's membrane (disorder)"
          },
          {
            "code": "37075008",
            "display": "Microcystoid retinal degeneration (disorder)"
          },
          {
            "code": "40787005",
            "display": "Conjunctival degeneration (disorder)"
          },
          {
            "code": "414173003",
            "display": "Exudative age-related macular degeneration (disorder)"
          },
          {
            "code": "414875008",
            "display": "Nonexudative age-related macular degeneration (disorder)"
          },
          {
            "code": "417939004",
            "display": "Amyloid corneal degeneration (disorder)"
          },
          {
            "code": "418871005",
            "display": "Spheroidal degeneration of conjunctiva (disorder)"
          },
          {
            "code": "419051009",
            "display": "Polymorphic amyloid degeneration of cornea (disorder)"
          },
          {
            "code": "419648001",
            "display": "Senile furrow degeneration of cornea (disorder)"
          },
          {
            "code": "424358006",
            "display": "Vitreoretinal tuft (disorder)"
          },
          {
            "code": "428212003",
            "display": "Photoreceptor degeneration (disorder)"
          },
          {
            "code": "450921000124103",
            "display": "Degeneration of cornea of right eye (disorder)"
          },
          {
            "code": "54184008",
            "display": "Senile reticular retinal degeneration (disorder)"
          },
          {
            "code": "60189009",
            "display": "Vitreous degeneration (disorder)"
          },
          {
            "code": "61536007",
            "display": "Peripheral retinal degeneration (disorder)"
          },
          {
            "code": "62585004",
            "display": "Degenerative disorder of eye (disorder)"
          },
          {
            "code": "679171000119109",
            "display": "Salzmann's nodular degeneration of cornea of bilateral eyes (disorder)"
          },
          {
            "code": "679181000119107",
            "display": "Salzmann nodular degeneration of cornea of left eye (disorder)"
          },
          {
            "code": "679191000119105",
            "display": "Salzmann nodular degeneration of cornea of right eye (disorder)"
          },
          {
            "code": "679201000119108",
            "display": "Pellucid marginal degeneration of cornea of bilateral eyes (disorder)"
          },
          {
            "code": "679211000119106",
            "display": "Terrien's marginal degeneration of peripheral cornea of bilateral eyes (disorder)"
          },
          {
            "code": "679221000119104",
            "display": "Pellucid marginal degeneration of cornea of left eye (disorder)"
          },
          {
            "code": "679231000119101",
            "display": "Terrien's marginal degeneration of peripheral cornea of left eye (disorder)"
          },
          {
            "code": "679241000119105",
            "display": "Pellucid marginal degeneration of cornea of right eye (disorder)"
          },
          {
            "code": "679251000119107",
            "display": "Terrien's marginal degeneration of peripheral cornea of right eye (disorder)"
          },
          {
            "code": "69134001",
            "display": "Paving stone retinal degeneration (disorder)"
          },
          {
            "code": "72620002",
            "display": "Nodular degeneration of cornea (disorder)"
          },
          {
            "code": "737271000",
            "display": "Subconjunctival degeneration (disorder)"
          },
          {
            "code": "770791000",
            "display": "Autosomal dominant neovascular inflammatory vitreoretinopathy (disorder)"
          },
          {
            "code": "83231000119101",
            "display": "Optic nerve and photoreceptor degeneration (disorder)"
          },
          {
            "code": "88538005",
            "display": "Calcareous degeneration of cornea (disorder)"
          },
          {
            "code": "89182000",
            "display": "Peripheral degeneration of cornea (disorder)"
          },
          {
            "code": "95695004",
            "display": "Degeneration of retina (disorder)"
          },
          {
            "code": "95696003",
            "display": "Glaucomatous retinal degeneration (disorder)"
          },
          {
            "code": "95697007",
            "display": "Generalized retinal degeneration (disorder)"
          },
          {
            "code": "95699005",
            "display": "Multifocal retinal degeneration (disorder)"
          },
          {
            "code": "95700006",
            "display": "Sudden acquired retinal degeneration (disorder)"
          }
        ]
      }
    ]
  },
  "expansion": {
    "identifier": "urn:uuid:509c8b1f-3a5e-4cda-acfe-ba317853792d",
    "timestamp": "2025-05-23T22:40:20-04:00",
    "total": 119,
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        "code": "15732881000119102",
        "display": "Generalized degeneration of retina of bilateral eyes (disorder)"
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        "code": "15732921000119109",
        "display": "Generalized degeneration of retina of left eye (disorder)"
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        "system": "http://snomed.info/sct",
        "version": "http://snomed.info/sct/731000124108/version/20250301",
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        "display": "Generalized degeneration of retina of right eye (disorder)"
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        "system": "http://snomed.info/sct",
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        "display": "Sudden acquired retinal degeneration (disorder)"
      }
    ]
  }
}