FHIR IG analytics| Package | hl7.fhir.us.uscdi-scd |
| Resource Type | ValueSet |
| Id | ValueSet-scd-diagnosis-vs.json |
| FHIR Version | R4 |
| Source | https://build.fhir.org/ig/hlnconsulting/uscdi-scd-ig/ValueSet-scd-diagnosis-vs.html |
| URL | http://hl7.org/fhir/us/uscdi-scd/ValueSet/scd-diagnosis-vs |
| Version | 0.1.0 |
| Status | active |
| Date | 2026-09-11T00:10:30+00:00 |
| Name | SCDDiagnosisVS |
| Title | SCD Diagnosis Value Set |
| Realm | us |
| Authority | hl7 |
| Description | Value set of codes representing the primary Sickle Cell Disease diagnoses, including all major genotypic subtypes. Intended for use with the SCDConditionProblemsAndHealthConcerns profile for the primary SCD diagnosis entry on a patient's problem list. Includes ICD-10-CM D57.x codes and equivalent SNOMED CT codes. TODO: Expand with complete SNOMED CT concept set and confirm ICD-10-CM code coverage. Submit to VSAC for OID assignment. |
| Copyright | ICD-10-CM codes are in the public domain. SNOMED CT codes require a SNOMED CT affiliate license. |
No resources found
| CodeSystem | ||
| fhir.tx.support#1.0.1 | icd-10-cm | International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) |
| hl7.fhir.uv.xver-r4.r4b#0.1.0 | sct | SNOMED CT (all versions) |
Note: links and images are rebased to the (stated) source
Generated Narrative: ValueSet scd-diagnosis-vs
This value set includes codes based on the following rules:
http://hl7.org/fhir/sid/icd-10-cm version Not Stated (use latest from terminology server)| Code | Display |
| D57.1 | Sickle-cell disease without crisis, Hb-SS |
| D57.00 | Hb-SS disease with crisis, unspecified |
| D57.01 | Hb-SS disease with acute chest syndrome |
| D57.02 | Hb-SS disease with splenic sequestration |
| D57.03 | Hb-SS disease with cerebral vascular involvement |
| D57.04 | Hb-SS disease with dactylitis |
| D57.09 | Hb-SS disease with crisis with other specified complication |
| D57.20 | Sickle-cell/Hb-C disease without crisis |
| D57.211 | Sickle-cell/Hb-C disease with acute chest syndrome |
| D57.212 | Sickle-cell/Hb-C disease with splenic sequestration |
| D57.213 | Sickle-cell/Hb-C disease with cerebral vascular involvement |
| D57.214 | Sickle-cell/Hb-C disease with dactylitis |
| D57.219 | Sickle-cell/Hb-C disease with crisis, unspecified |
| D57.40 | Sickle-cell thalassemia, unspecified, without crisis |
| D57.411 | Sickle-cell thalassemia, unspecified, with acute chest syndrome |
| D57.412 | Sickle-cell thalassemia, unspecified, with splenic sequestration |
| D57.419 | Sickle-cell thalassemia, unspecified, with crisis |
| D57.42 | Sickle-cell thalassemia beta zero without crisis |
| D57.431 | Sickle-cell thalassemia beta zero with acute chest syndrome |
| D57.432 | Sickle-cell thalassemia beta zero with splenic sequestration |
| D57.439 | Sickle-cell thalassemia beta zero with crisis, unspecified |
| D57.44 | Sickle-cell thalassemia beta plus without crisis |
| D57.451 | Sickle-cell thalassemia beta plus with acute chest syndrome |
| D57.452 | Sickle-cell thalassemia beta plus with splenic sequestration |
| D57.459 | Sickle-cell thalassemia beta plus with crisis, unspecified |
| D57.80 | Other sickle-cell disorders without crisis |
| D57.811 | Other sickle-cell disorders with acute chest syndrome |
| D57.812 | Other sickle-cell disorders with splenic sequestration |
| D57.819 | Other sickle-cell disorders with crisis, unspecified |
http://snomed.info/sct version Not Stated (use latest from terminology server)| Code | Display |
| 127040003 | Sickle cell-hemoglobin SS disease (disorder) |
| 416180004 | Sickle cell-hemoglobin C disease (disorder) |
| 417571000 | Sickle cell-beta-zero-thalassemia (disorder) |
| 417425009 | Sickle cell-beta-plus-thalassemia (disorder) |
| 417748003 | Sickle cell-hemoglobin D disease (disorder) |
| 417279003 | Sickle cell-hemoglobin E disease (disorder) |
| 444751005 | Hemoglobin S-O Arab disease (disorder) |
| 35434009 | Sickle cell disorder (disorder) |
{
"resourceType": "ValueSet",
"id": "scd-diagnosis-vs",
"text": {
"status": "generated",
"div": "<!-- snip (see above) -->"
},
"url": "http://hl7.org/fhir/us/uscdi-scd/ValueSet/scd-diagnosis-vs",
"version": "0.1.0",
"name": "SCDDiagnosisVS",
"title": "SCD Diagnosis Value Set",
"status": "active",
"experimental": false,
"date": "2026-09-11T00:10:30+00:00",
"publisher": "HL7 International / Public Health",
"contact": [
{
"name": "HL7 International / Public Health",
"telecom": [
{
"system": "url",
"value": "https://www.hl7.org/Special/committees/pher"
},
{
"system": "email",
"value": "pher@lists.HL7.org"
}
]
},
{
"name": "HL7 Public Health Work Group",
"telecom": [
{
"system": "url",
"value": "http://www.hl7.org/Special/committees/pher"
},
{
"system": "email",
"value": "pher@lists.HL7.org"
}
]
}
],
"description": "Value set of codes representing the primary Sickle Cell Disease diagnoses,\nincluding all major genotypic subtypes. Intended for use with the\nSCDConditionProblemsAndHealthConcerns profile for the primary SCD diagnosis\nentry on a patient's problem list.\n\nIncludes ICD-10-CM D57.x codes and equivalent SNOMED CT codes.\n\nTODO: Expand with complete SNOMED CT concept set and confirm ICD-10-CM\ncode coverage. Submit to VSAC for OID assignment.",
"jurisdiction": [
{
"coding": [
{
"system": "urn:iso:std:iso:3166",
"code": "US",
"display": "United States of America"
}
]
}
],
"copyright": "ICD-10-CM codes are in the public domain. SNOMED CT codes require a SNOMED CT affiliate license.",
"compose": {
"include": [
{
"system": "http://hl7.org/fhir/sid/icd-10-cm",
"concept": [
{
"code": "D57.1",
"display": "Sickle-cell disease without crisis, Hb-SS"
},
{
"code": "D57.00",
"display": "Hb-SS disease with crisis, unspecified"
},
{
"code": "D57.01",
"display": "Hb-SS disease with acute chest syndrome"
},
{
"code": "D57.02",
"display": "Hb-SS disease with splenic sequestration"
},
{
"code": "D57.03",
"display": "Hb-SS disease with cerebral vascular involvement"
},
{
"code": "D57.04",
"display": "Hb-SS disease with dactylitis"
},
{
"code": "D57.09",
"display": "Hb-SS disease with crisis with other specified complication"
},
{
"code": "D57.20",
"display": "Sickle-cell/Hb-C disease without crisis"
},
{
"code": "D57.211",
"display": "Sickle-cell/Hb-C disease with acute chest syndrome"
},
{
"code": "D57.212",
"display": "Sickle-cell/Hb-C disease with splenic sequestration"
},
{
"code": "D57.213",
"display": "Sickle-cell/Hb-C disease with cerebral vascular involvement"
},
{
"code": "D57.214",
"display": "Sickle-cell/Hb-C disease with dactylitis"
},
{
"code": "D57.219",
"display": "Sickle-cell/Hb-C disease with crisis, unspecified"
},
{
"code": "D57.40",
"display": "Sickle-cell thalassemia, unspecified, without crisis"
},
{
"code": "D57.411",
"display": "Sickle-cell thalassemia, unspecified, with acute chest syndrome"
},
{
"code": "D57.412",
"display": "Sickle-cell thalassemia, unspecified, with splenic sequestration"
},
{
"code": "D57.419",
"display": "Sickle-cell thalassemia, unspecified, with crisis"
},
{
"code": "D57.42",
"display": "Sickle-cell thalassemia beta zero without crisis"
},
{
"code": "D57.431",
"display": "Sickle-cell thalassemia beta zero with acute chest syndrome"
},
{
"code": "D57.432",
"display": "Sickle-cell thalassemia beta zero with splenic sequestration"
},
{
"code": "D57.439",
"display": "Sickle-cell thalassemia beta zero with crisis, unspecified"
},
{
"code": "D57.44",
"display": "Sickle-cell thalassemia beta plus without crisis"
},
{
"code": "D57.451",
"display": "Sickle-cell thalassemia beta plus with acute chest syndrome"
},
{
"code": "D57.452",
"display": "Sickle-cell thalassemia beta plus with splenic sequestration"
},
{
"code": "D57.459",
"display": "Sickle-cell thalassemia beta plus with crisis, unspecified"
},
{
"code": "D57.80",
"display": "Other sickle-cell disorders without crisis"
},
{
"code": "D57.811",
"display": "Other sickle-cell disorders with acute chest syndrome"
},
{
"code": "D57.812",
"display": "Other sickle-cell disorders with splenic sequestration"
},
{
"code": "D57.819",
"display": "Other sickle-cell disorders with crisis, unspecified"
}
]
},
{
"system": "http://snomed.info/sct",
"concept": [
{
"code": "127040003",
"display": "Sickle cell-hemoglobin SS disease (disorder)"
},
{
"code": "416180004",
"display": "Sickle cell-hemoglobin C disease (disorder)"
},
{
"code": "417571000",
"display": "Sickle cell-beta-zero-thalassemia (disorder)"
},
{
"code": "417425009",
"display": "Sickle cell-beta-plus-thalassemia (disorder)"
},
{
"code": "417748003",
"display": "Sickle cell-hemoglobin D disease (disorder)"
},
{
"code": "417279003",
"display": "Sickle cell-hemoglobin E disease (disorder)"
},
{
"code": "444751005",
"display": "Hemoglobin S-O Arab disease (disorder)"
},
{
"code": "35434009",
"display": "Sickle cell disorder (disorder)"
}
]
}
]
}
}