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Packagefhir.cdc.opioid-cds-r4
Resource TypeValueSet
IdValueSet-sickle-cell-diseases.json
FHIR VersionR4
Sourcehttps://build.fhir.org/ig/cqframework/opioid-cds-r4/ValueSet-sickle-cell-diseases.html
URLhttp://fhir.org/guides/cdc/opioid-cds/ValueSet/sickle-cell-diseases
Version2022.1.0
Statusactive
Date2023-05-25T18:08:12-06:00
NameSICKLE_CELL_DISEASES
TitleSickle-cell diseases
Realmus
Authorityhl7
DescriptionSickle-cell disorders that cause painful crisis
PurposeConditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations
Copyright© CDC 2016+.

Resources that use this resource

StructureDefinition
SickleCellEncounterDiagnosisConditionSickle Cell Encounter Diagnosis Condition Profile
SickleCellProblemListHealthConcernConditionSickle Cell Problem List Health Concern Condition Profile

Resources that this resource uses

CodeSystem
icd-10-cmInternational Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM)
sctSNOMED codes used in this IG

Narrative

Note: links and images are rebased to the (stated) source

Generated Narrative: ValueSet sickle-cell-diseases

Expansion based on:

  • codesystem International Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM) version 2024
  • SNOMED CT United States edition 01-Sep 2024

This value set expansion contains 81 concepts.

SystemCodeDisplay
http://snomed.info/sct  417357006Sickling disorder due to hemoglobin S (disorder)
http://snomed.info/sct  23269001Double heterozygous sickling disorder
http://snomed.info/sct  25472008Sickle cell-hemoglobin D disease
http://snomed.info/sct  35434009Sickle cell-hemoglobin C disease
http://snomed.info/sct  36472007Hemoglobin S-F disease
http://snomed.info/sct  47024008Sickle cell-hemoglobin E disease
http://snomed.info/sct  127040003Sickle cell anemia
http://snomed.info/sct  127041004Sickle cell-beta-thalassemia
http://snomed.info/sct  127042006Sickle cell beta plus thalassaemia
http://snomed.info/sct  127043001Sickle cell-beta^0^-thalassemia
http://snomed.info/sct  127044007Sickle cell-delta beta^0^-thalassemia
http://snomed.info/sct  127045008Sickle cell anemia with coexistent alpha-thalassemia
http://snomed.info/sct  127047000Sickle cell-hemoglobin Lepore disease
http://snomed.info/sct  127048005Sickle cell-Hemoglobin O Arab disease
http://snomed.info/sct  234391009Sickle cell anemia with high hemoglobin F
http://snomed.info/sct  416484003Sickle cell-hemoglobin E disease with crisis (disorder)
http://snomed.info/sct  416826005Sickle cell-thalassemia disease with crisis (disorder)
http://snomed.info/sct  417048006Sickle cell-thalassemia disease without crisis (disorder)
http://snomed.info/sct  417279003Hemoglobin S sickling disorder with crisis (disorder)
http://snomed.info/sct  417425009Hemoglobin SS disease with crisis (disorder)
http://snomed.info/sct  417517009Sickle cell-hemoglobin C disease with crisis (disorder)
http://snomed.info/sct  417748003Sickle cell-hemoglobin D disease with crisis (disorder)
http://snomed.info/sct  440206000Hemoglobin SS disease with vasoocclusive crisis (disorder)
http://snomed.info/sct  444108000Acute sickle cell splenic sequestration crisis (disorder)
http://snomed.info/sct  783254003Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome
http://snomed.info/sct  1153413001Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)
http://snomed.info/sct  1153415008Acute splenic sequestration due to sickle cell hemoglobin C disease with crisis
http://snomed.info/sct  10759351000119103Sickle cell anaemia in mother complicating childbirth
http://snomed.info/sct  441482006History of sickle cell anaemia
http://hl7.org/fhir/sid/icd-10-cm  D57Sickle-cell disorders
http://hl7.org/fhir/sid/icd-10-cm  D57.0Hb-SS disease with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.00Hb-SS disease with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.01Hb-SS disease with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.02Hb-SS disease with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.03Hb-SS disease with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.04Hb-SS disease with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.09Hb-SS disease with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.2Sickle-cell/Hb-C disease
http://hl7.org/fhir/sid/icd-10-cm  D57.20Sickle-cell/Hb-C disease without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.21Sickle-cell/Hb-C disease with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.211Sickle-cell/Hb-C disease with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.212Sickle-cell/Hb-C disease with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.213Sickle-cell/Hb-C disease with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.214Sickle-cell/Hb-C disease with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.218Sickle-cell/Hb-C disease with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.219Sickle-cell/Hb-C disease with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.3Sickle-cell trait
http://hl7.org/fhir/sid/icd-10-cm  D57.4Sickle-cell thalassemia
http://hl7.org/fhir/sid/icd-10-cm  D57.40Sickle-cell thalassemia without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.41Sickle-cell thalassemia, unspecified, with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.411Sickle-cell thalassemia, unspecified, with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.412Sickle-cell thalassemia, unspecified, with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.413Sickle-cell thalassemia, unspecified, with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.414Sickle-cell thalassemia, unspecified, with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.418Sickle-cell thalassemia, unspecified, with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.419Sickle-cell thalassemia, unspecified, with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.42Sickle-cell thalassemia beta zero without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.43Sickle-cell thalassemia beta zero with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.431Sickle-cell thalassemia beta zero with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.432Sickle-cell thalassemia beta zero with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.433Sickle-cell thalassemia beta zero with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.434Sickle-cell thalassemia beta zero with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.438Sickle-cell thalassemia beta zero with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.439Sickle-cell thalassemia beta zero with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.44Sickle-cell thalassemia beta plus without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.45Sickle-cell thalassemia beta plus with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.451Sickle-cell thalassemia beta plus with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.452Sickle-cell thalassemia beta plus with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.453Sickle-cell thalassemia beta plus with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.454Sickle-cell thalassemia beta plus with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.458Sickle-cell thalassemia beta plus with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.459Sickle-cell thalassemia beta plus with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.8Other sickle-cell disorders
http://hl7.org/fhir/sid/icd-10-cm  D57.80Other sickle-cell disorders without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.81Other sickle-cell disorders with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.811Other sickle-cell disorders with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.812Other sickle-cell disorders with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.813Other sickle-cell disorders with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.814Other sickle-cell disorders with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.818Other sickle-cell disorders with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.819Other sickle-cell disorders with crisis, unspecified

Source1

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  "purpose": "Conditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations",
  "copyright": "© CDC 2016+.",
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        "system": "http://snomed.info/sct",
        "code": "417357006",
        "display": "Sickling disorder due to hemoglobin S (disorder)"
      },
      {
        "system": "http://snomed.info/sct",
        "code": "23269001",
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        "display": "Sickle cell-hemoglobin E disease"
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        "code": "127047000",
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      },
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        "code": "127048005",
        "display": "Sickle cell-Hemoglobin O Arab disease"
      },
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        "system": "http://snomed.info/sct",
        "code": "234391009",
        "display": "Sickle cell anemia with high hemoglobin F"
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        "system": "http://snomed.info/sct",
        "code": "416484003",
        "display": "Sickle cell-hemoglobin E disease with crisis (disorder)"
      },
      {
        "system": "http://snomed.info/sct",
        "code": "416826005",
        "display": "Sickle cell-thalassemia disease with crisis (disorder)"
      },
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        "system": "http://snomed.info/sct",
        "code": "417048006",
        "display": "Sickle cell-thalassemia disease without crisis (disorder)"
      },
      {
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        "code": "417279003",
        "display": "Hemoglobin S sickling disorder with crisis (disorder)"
      },
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        "code": "417425009",
        "display": "Hemoglobin SS disease with crisis (disorder)"
      },
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        "code": "417517009",
        "display": "Sickle cell-hemoglobin C disease with crisis (disorder)"
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        "code": "417748003",
        "display": "Sickle cell-hemoglobin D disease with crisis (disorder)"
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        "display": "Hemoglobin SS disease with vasoocclusive crisis (disorder)"
      },
      {
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        "display": "Acute sickle cell splenic sequestration crisis (disorder)"
      },
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        "code": "783254003",
        "display": "Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome"
      },
      {
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        "display": "Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)"
      },
      {
        "system": "http://snomed.info/sct",
        "code": "1153415008",
        "display": "Acute splenic sequestration due to sickle cell hemoglobin C disease with crisis"
      },
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        "code": "10759351000119103",
        "display": "Sickle cell anaemia in mother complicating childbirth"
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        "display": "Hb-SS disease with crisis"
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      {
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        "display": "Hb-SS disease with crisis, unspecified"
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      {
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        "code": "D57.01",
        "display": "Hb-SS disease with acute chest syndrome"
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      {
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        "code": "D57.02",
        "display": "Hb-SS disease with splenic sequestration"
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      {
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        "code": "D57.03",
        "display": "Hb-SS disease with cerebral vascular involvement"
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      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.04",
        "display": "Hb-SS disease with dactylitis"
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      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.09",
        "display": "Hb-SS disease with crisis with other specified complication"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.2",
        "display": "Sickle-cell/Hb-C disease"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.20",
        "display": "Sickle-cell/Hb-C disease without crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.21",
        "display": "Sickle-cell/Hb-C disease with crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.211",
        "display": "Sickle-cell/Hb-C disease with acute chest syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.212",
        "display": "Sickle-cell/Hb-C disease with splenic sequestration"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.213",
        "display": "Sickle-cell/Hb-C disease with cerebral vascular involvement"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.214",
        "display": "Sickle-cell/Hb-C disease with dactylitis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.218",
        "display": "Sickle-cell/Hb-C disease with crisis with other specified complication"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.219",
        "display": "Sickle-cell/Hb-C disease with crisis, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.3",
        "display": "Sickle-cell trait"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.4",
        "display": "Sickle-cell thalassemia"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.40",
        "display": "Sickle-cell thalassemia without crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.41",
        "display": "Sickle-cell thalassemia, unspecified, with crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.411",
        "display": "Sickle-cell thalassemia, unspecified, with acute chest syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.412",
        "display": "Sickle-cell thalassemia, unspecified, with splenic sequestration"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.413",
        "display": "Sickle-cell thalassemia, unspecified, with cerebral vascular involvement"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.414",
        "display": "Sickle-cell thalassemia, unspecified, with dactylitis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.418",
        "display": "Sickle-cell thalassemia, unspecified, with crisis with other specified complication"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.419",
        "display": "Sickle-cell thalassemia, unspecified, with crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.42",
        "display": "Sickle-cell thalassemia beta zero without crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.43",
        "display": "Sickle-cell thalassemia beta zero with crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.431",
        "display": "Sickle-cell thalassemia beta zero with acute chest syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.432",
        "display": "Sickle-cell thalassemia beta zero with splenic sequestration"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.433",
        "display": "Sickle-cell thalassemia beta zero with cerebral vascular involvement"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.434",
        "display": "Sickle-cell thalassemia beta zero with dactylitis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.438",
        "display": "Sickle-cell thalassemia beta zero with crisis with other specified complication"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.439",
        "display": "Sickle-cell thalassemia beta zero with crisis, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.44",
        "display": "Sickle-cell thalassemia beta plus without crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.45",
        "display": "Sickle-cell thalassemia beta plus with crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.451",
        "display": "Sickle-cell thalassemia beta plus with acute chest syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.452",
        "display": "Sickle-cell thalassemia beta plus with splenic sequestration"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.453",
        "display": "Sickle-cell thalassemia beta plus with cerebral vascular involvement"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.454",
        "display": "Sickle-cell thalassemia beta plus with dactylitis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.458",
        "display": "Sickle-cell thalassemia beta plus with crisis with other specified complication"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.459",
        "display": "Sickle-cell thalassemia beta plus with crisis, unspecified"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.8",
        "display": "Other sickle-cell disorders"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.80",
        "display": "Other sickle-cell disorders without crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.81",
        "display": "Other sickle-cell disorders with crisis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.811",
        "display": "Other sickle-cell disorders with acute chest syndrome"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.812",
        "display": "Other sickle-cell disorders with splenic sequestration"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.813",
        "display": "Other sickle-cell disorders with cerebral vascular involvement"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.814",
        "display": "Other sickle-cell disorders with dactylitis"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.818",
        "display": "Other sickle-cell disorders with crisis with other specified complication"
      },
      {
        "system": "http://hl7.org/fhir/sid/icd-10-cm",
        "code": "D57.819",
        "display": "Other sickle-cell disorders with crisis, unspecified"
      }
    ]
  }
}